Anomalies associated with the development of urinarypathways constitute more than 35% of all congenital malformations in humans. At the same time, there are cases when such pathologies are asymptomatic and are determined only during puberty or pregnancy. Frehlie syndrome is an abnormality of the kidneys of a congenital nature, at which the junction of the anterior and posterior branches of the superior renal artery is formed. As a result, the normal functions of the organ are disrupted.
The name of the syndrome was named after the American urologist, who first described it. The article deals with the causes, symptoms and treatment of the disease.
As already mentioned, with fraili syndromethe posterior and anterior branches of the renal artery intersect. At the same time partial compression of the upper parts of the pelvis or pelvic-ureteric segment is possible. As a result, kidney function may be impaired or completely lost. There is a likelihood of stone formation, the appearance of hypertension. Traces of blood may be found in the urine.
A similar anomaly occurs even in the course of embryogenesis of the vascular system of the kidneys, when it is possible to stop their development, but preserve the structures.
Localized frayli syndrome right and left, thenthere is usually one kidney affected. In extreme cases, both organs may suffer. In this case, the syndrome may be accompanied by a defect in the filling of the upper group of cups and right-side or left-sided pyeloectasia due to obstruction of the ureter.
There are some signs indirectlyindicating that the patient may have fraili syndrome. Symptoms appear tangible pain in the lumbar region, renal colic, which are present in connection with secondary nephrolithiasis. In addition, there is slight hypertension, as well as macro- and microhematuria.
The most difficult to clinically diagnose fraule syndromesmall, especially in infants. For the correct diagnosis using the method of renal vascular Doppler sonography, also used multislice computed tomography.
It is difficult for babies to carry out angiographic studies, so at present they are almost never used.
In addition to the above methods for patientsprescribe urine and blood tests, including sensitivity to drugs and flora. In addition, ultrasound of the urinary system is performed.
The treatment of this disease is prescribed onlyafter a thorough due diligence and confirmation of the diagnosis. The conservative method - antihypertensive therapy - is used in rare cases. It is directed, as a rule, to decrease in pressure in the event that it is raised. They also conduct a set of measures to eliminate secondary pyelonephritis and are involved in the prevention of urolithiasis.
However, the safest way to completely eliminateFrehley syndrome is not a conservative treatment, but a surgical one. During the operation, the doctor removes the crossing of the arteries in the kidneys and the pressure on them stops.
In any case, patients (and especially babies)one should register with a nephrologist and get his consultations regularly, take the necessary tests, undergo ultrasound and radiographic examinations. In later life, Fraulee syndrome may not manifest itself at all, the degree of discomfort depends on how severely the renal pelvis is trapped. With a healthy lifestyle and the absence of bad habits, patients may not feel any symptoms at all.
Беременность и рождение ребенка при синдроме Mothers pass through only under the supervision of a specialist. As a rule, women with congenital malformations of the kidneys, which include this syndrome, are allowed to bear the fetus only after surgery. The fact is that Frehlie's syndrome is often accompanied by an increase in blood pressure, pregnancy in this case is more difficult, sometimes it has to be interrupted for a period after 22 weeks.
But even after successful surgery and recoverykidney function, a pregnant woman should be warned about this by her obstetrician-gynecologist. The patient is obliged to be under the supervision of a nephrologist for the entire period of childbearing, periodically undergo tests, undergo tests and, if necessary, be hospitalized.
Very often, exacerbation of kidney disease canappear for a period of 15-16 or 26-30 weeks. Symptoms are a delayed discharge of urine, severe swelling of the arms and legs, pain and discomfort during urination. In later periods, complications are possible due to the rapidly growing uterus, which puts pressure on the ureters. In the event of the appearance of such signs of a pregnant woman with Freyla syndrome, urgent hospitalization is necessary.
Very often, kidney defects are an indication for cesarean section. However, the threat to the child in this case is negligible.
For pregnant women with Fraely syndrome and othersmalformations of the kidneys are specialized maternity hospitals, in the staff of which urologists and nephrologists are necessarily present, and a newborn baby immediately after birth comes a comprehensive examination.
So, in the article was considered such a disease.kidney like frayli syndrome. Despite the fact that the anomaly is congenital, it is currently treatable successfully, and patients after surgery may return to a normal lifestyle.
